(John Bruce Beckwith, born1933, American pathologist; Hans Rudolf Wiedemann, born 1915, German paediatrician).The clinical features are macroglossia, visceromegaly, umbilical hernia and hypoglycaemia. There is an increased incidence of Wilms tumour. Ultrasound examination confirms the visceromegaly which mainly affects the kidneys and liver. The umbilical hernia is visible on plain abdominal radiographs.The associated neoplasms affect the kidneys and liver.